A rare case of VACTERL association at the Federal Medical Centre, Yenagoa, Bayelsa State, Nigeria.

Okpara LA1, Oriji PC1*, Obagah L1
1Department of Obstetrics and Gynaecology, Federal Medical Centre, Yenagoa, Bayelsa State, Nigeria.
*Correspondence: Dr. Oriji, Peter Chibuzor; +234 706 423 3209; chibuzor54@gmail.com

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Abstract

Background: VACTERL association is a condition comprising multisystemic congenital malformations, causing severe physical disability in affected individuals and is usually a great burden to the family and challenging for the paediatrician. VACTERL/VACTER is characterized by presence of vertebral defects, anal atresia, cardiac defects, trachea-oesophageal fistula, renal anomalies and limb abnormalities.
Case presentation: A live male baby was delivered at the labour ward of the Federal Medical Centre, Yenagoa, following preterm pre-labour rupture of foetal membranes at 30 weeks’ gestational age with multiple congenital malformations. The neonate was immediately transferred to the special care baby unit (SCBU) of the facility for expert care. Baby died within four hours of life.
Conclusion: VACTERL association is a very rare congenital anomaly. Aetiology is unknown and diagnosis is made on clinical picture. Management is quite challenging and multidisciplinary approach is needed to optimize neonatal survival.

Keywords: VACTERL association, Congenital malformations, Multidisciplinary.

Cite this article: Okpara LA, Oriji PC, Obagah L. A rare case of VACTERL association at the Federal Medical Centre, Yenagoa, Bayelsa State, Nigeria. Yen Med J. 2020;2(2):81–83.

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