Asymptomatic right-sided aortic arch in a Nigerian woman: a case report and literature review.

Idowu BM1*
1Department of Radiology, Union Diagnostics and Clinical Services, 37, Tejuosho Street, Yaba, Lagos State, Nigeria.
*Correspondence: Dr. Idowu, Bukunmi Michael; ibmcontacts@gmail.com

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Abstract

Background: Right-sided aortic arch (RAA) is a rare congenital anomaly of the cardiovascular system that stems from the persistence of the right fourth branchial arch. It occurs in < 0.1% of the population. RAA with an aberrant left subclavian artery is the most frequent type. The associated aberrant left subclavian artery occurs in about 50% of RAA cases. Anomalies of the great arteries (e.g., Fallot’s tetralogy) are common when RAA occurs in a normal visceral situs setting. By contrast, some cases of RAA remain asymptomatic throughout life. Echocardiography, multidetector cardiac CT, cardiac MRI, and cardiac catheterisation are the cornerstone of investigation in RAA cases.
Case presentation: This is a case report of an asymptomatic right-sided aortic arch without associated congenital anomalies detected incidentally in an adult during a pre-employment medical examination. The patient was symptomless; therefore, no treatment was given.
Conclusion: Very few cases of RAA in adults are entirely asymptomatic, as reported in this case. A review of the literature yielded scanty reports of aortic arch anomalies among Nigerians (paediatric and adults). In the previous decade (2011–2020), there were at least 32 case reports of RAA in adults. Of this number, only one was completely asymptomatic like this case report. This report might be the first documentation of an asymptomatic isolated RAA in a Nigerian.

Keywords: Right-sided aortic arch, Aortic arch variant, Cardiovascular anomalies, Computerised tomography, Case report.

Cite this article: Idowu BM. Asymptomatic right-sided aortic arch in a Nigerian woman: a case report and literature review. Yen Med J. 2021;3(1):148–152.

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